Table 1 Distribution prevalence of Critical Congenital Heart Defects types with their ICD-10 codes, Turkey, 2018–2020 (n = 9884)
CCHD type | ICD-10 | CCHD, n (%)* | Prevalence of CCHD (1/10,000 live birth) |
|---|---|---|---|
Overall | 9884 (100.0) | 27.8 | |
Group 1 diseases | 4392 (44.4) | ||
Tetralogy of Fallot | Q21.3 | 1721 (17.4) | 4.8 |
Hypoplastic left heart syndrome | Q23.4 | 929 (9.4) | 2.6 |
Transposition of great arteries | Q20.3 | 825 (8.3) | 2.3 |
Total anomalous pulmonary venous return | Q26.2 | 388 (3.9) | 1.1 |
Pulmonary atresia with intact ventricular septum | Q22.0 | 200 (2.0) | 0.6 |
Truncus arteriosus | Q20.0 | 199 (2.0) | 0.6 |
Tricuspid atresia | Q22.4 | 130 (1.3) | 0.4 |
Group 2 diseases | 5415 (54.8) | 15.2 | |
Aortic arch anomalies ** | Q25.1,Q25.2, Q25.4 | 2098 (21.2) | 5.9 |
Atrioventricular septal defect | Q21.2 | 2021 (20.4) | 5.7 |
Pulmonary valve stenosis | Q22.1 | 672 (6.8) | 1.9 |
Single ventricle physiology diseases *** | Q20.1, Q20.2, Q20.4, Q22.6 | 490 (5.0) | 1.4 |
Ebstein anomaly | Q22.5 | 134 (1.4) | 0.4 |
Ungrouped | 77 (0.8) | 0.2 |