Table 2 Concomitant anomalies in complicated PRUV cases

Cardiovascular

41

Ventricular septal defect

10

Persistent left superior vena cava

9

Single ventricle

7

Complete atrioventricular canal defect

6

Common arterial trunk

6

Transposition of the great arteries

6

Right-sided aortic arch

4

Tetralogy of Fallot

4

Pulmonary artery stenosis

3

Aberrant left subclavian artery

2

Dextroversion of heart

2

Double outlet right ventricle

1

Right heart enlargement, tricuspid valve regurgitation

1

Dextrocardia

1

Interrupted aortic arch

1

Hypoplastic left heart

1

Atrial septal defect

1

Pulmonary artery valve stenosis

1

Total anomalous pulmonary venous return

1

Nervous system

20

Spina bifida

5

Choroid plexus cyst

5

Hydrocephalus

3

Cerebellar vermis agenesis, incomplete development

2

Vein of Galen malformation

2

Posterior fossa effusion

1

Lateral ventricular dilatation

1

Bilateral ependymal cyst

1

Bilateral lateral intraventricular hemorrhage

1

Agenesis of the corpus callosum

1

Anencephaly

1

Urinary system

17

Unilateral or bilateral hydronephrosis

5

Unilateral duplex kidney or double pelvis

3

Unilateral or bilateral renal agenesis

3

Unilateral multicystic dysplastic kidney

3

Right renal hypoplasia

1

Ectopic kidney in right pelvic cavity

1

Right renal cyst

1

Ureterocele

1

Bilateral renal echo enhancement

1

Skeletal system

17

Shortened limbs

8

Unilateral or bilateral club hand

5

Bilateral clubfoot

2

Unilateral shortened ulna and radius

2

Agenesis of right upper arm and forearm (right hand directly connected to shoulder joint)

1

Hemivertebrae

1

Butterfly vertebrae

1

Digestive system

5

Stenosis or atresia of small bowel

2

Esophageal atresia

2

Intestinal duplication

1

Respiratory system

4

Pulmonary cystic adenomatoid malformation

1

Pulmonary sequestration

1

Left lung agenesis

1

Left lung dysplasia

1

Other anomalies

29

Diaphragmatic hernia

5

Cleft lip and palate

3

Choledochal cyst

3

Ovarian cyst

3

Intestinal echo enhancement

3

Fetal intraabdominal umbilical vein varix

2

IUGR

2

Umbilical cord cyst

2

Intrauterine fetal death

1

Mandibular hypoplasia

1

Cystic teratoma in abdominal cavity

1

Orbital hypertelorism

1

Short umbilical cord

1

Acromphalus

1

Hepatic cyst

1

Multiple echo enhancement foci in gallbladder

1

Intrahepatic bile duct dilatation

1