Skip to main content

Table 1 Ultrasound appearance and outcomes of fetal unilateral lung agenesis with cardiac malposition in the current series

From: Prenatal diagnosis of fetal unilateral lung agenesis complicated with cardiac malposition

Case

GA

Lung agenesis

Cardiac position

Cardiac axis

CHD

Visualization of the PA

Postnatal confirmation

1

18

Left

Left

left axis 100°

None

MPA and RPA

Yes by CDE and DR

2

33

Left

Left

left axis 60°

None

MPA and RPA

Yes by CDE and CT

3

27

Left

Left

left axis 120°

None

MPA and RPA

Yes by autopsy

4

31

Left

Left

left axis 70°

Common ventricle and Primum ASD

MPA and RPA

Yes by autopsy

5

21

Left

Left

left axis 80°

DORV and VSD

MPA and RPA

Yes by autopsy

6

31

Left

Left

left axis 60°

VSD and TGA

MPA and RPA

Yes by autopsy

7

25

Left

Left

left axis 80°

VSD

MPA and RPA

Yes by CDE

8

26

Right

Right

right axis 50°

None

MPA and LPA

Yes by CDE, DR and CT

9

32

Right

Right

right axis 50°

None

MPA and LPA

Yes by CDE, DR, and CT

10

23

Right

Right

right axis 70°

None

MPA and LPA

Yes by CDE and DR

11

35

Right

Right

right axis 60°

None

MPA and LPA

Yes by CDE and CT

12

26

Right

Right

right axis 70°

None

MPA and LPA

Yes by CDE and CT

13

32

Right

Right

right axis 80°

None

MPA

Yes by CDE, DR and CT

14

35

Right

Right

right axis 50°

None

MPA and LPA

Yes by CDE, DR and CT

15

22

Right

Right

right axis 80°

None

MPA and LPA

Yes by CDE and CT

16

35

Right

Right

right axis 60°

AVSD

MPA and LPA

Yes by autopsy

17

27

Right

Right

right axis 60°

ccTGA and VSD

MPA and LPA

Yes by autopsy

18

28

Right

Right

right axis 60°

TGA and VSD

MPA and LPA

Yes by autopsy

  1. ASD, atrial septal defect; AVSD, atrioventricular septal defect; ccTGA, congenital corrected transposition of the great arteries; CDE, color Doppler echocardiography; CHD, congenital heart disease; CT, computed tomography; DORV, double outlet right ventricle; DR, digital radiography; GA, gestational age at examination (in weeks); LPA, left pulmonary artery; MPA, main pulmonary artery; PA, pulmonary artery; RPA, right pulmonary artery; TGA, transposition of the great arteries; VSD, ventricular septal defect.